What happens to the femoral head
The head of the femur in a child is fed by thin vessels running along the femoral neck. If blood flow through them is interrupted, the bone tissue under the cartilage dies. At the same time, the cartilage continues to receive nutrition from the joint fluid and remains alive, so the joint is not destroyed immediately. Then the body begins to resorb the dead bone and replace it with a new one - during this period the head is soft and easily flattens under the weight of the body. When the restructuring is completed, the shape of the head is finally fixed. That is why treatment is not aimed at “accelerating fusion”, but at protecting the head from stress during vulnerable months.
- Stage of necrosis - death of bone tissue, complaints may be minimal
- The fragmentation stage is the most vulnerable, the head is the easiest to deform
- Recovery stage - growth of new bone
- Outcome stage - the shape of the joint is fixed
- The entire cycle usually takes from 2 to 4 years
Causes and risk factors
The exact cause of Perthes disease is unknown. They discuss the structural features of blood vessels in children of this age, repeated microtraumas, blood clotting disorders and the influence of external factors. The disease is not contagious and is not directly inherited, although it is more common in some families. It is important for parents to know: the disease does not occur due to “lack of calcium” and not because the child ran a lot, so the feeling of guilt is inappropriate here, but the implementation of the exercise regime really affects the outcome.
- Ages 4–10 years, peak around 5–7 years
- Boys get sick several times more often than girls
- Delayed bone age and short stature
- Passive smoking in the family
- Repeated episodes of pain and synovitis in the joint
- Blood clotting disorders (discussed as a factor)
Symptoms: what to look out for
The disease begins unnoticed. The child begins to limp, especially in the evening and after an active day, and the pain is often felt not in the hip, but in the knee - this is referred pain along the obturator nerve. Therefore, any long-term knee pain in a child should be checked along with the hip joint. Abduction and internal rotation of the leg are gradually limited, the muscles of the thigh and buttocks become thinner, and the leg may seem a little shorter.
- Lameness that gets worse towards the end of the day
- Pain in the knee, groin, or outer thigh
- Limitation of hip abduction and internal rotation
- Reduction in the volume of the thigh and buttock muscles
- The child gets tired faster and asks to be held
- Complaints either intensify or disappear completely for weeks
Diagnostics
The basis of the diagnosis is an x-ray of the pelvis in a direct projection and in the abduction position: it shows the stage of the process, the size of the affected area and the condition of the roof of the acetabulum. In the earliest stages, x-rays are normal, then MRI of the hip joints helps, which sees the area of impaired blood supply earlier. Ultrasound reveals joint effusion and helps distinguish Perthes disease from transient synovitis. Blood tests are needed to rule out infectious arthritis and inflammatory joint diseases.
- X-ray of the pelvis in two projections, including the Lauenstein position
- MRI of the hip joints in early and controversial cases
- Ultrasound of the joint to assess effusion
- Complete blood count and C-reactive protein if infection is suspected
- Repeated images over time to control the stage
Treatment and prognosis
The goal of treatment is to keep the femoral head inside the acetabulum while it is soft and maintain joint mobility. In children under six years of age with minor lesions, observation, restriction of jumping and running, physical therapy and swimming are often sufficient. For larger lesions, abductor orthoses, plaster casts, traction are used, and for persistent deformity and limitation of movements, operations on the femur or pelvis are used. Painkillers and anti-inflammatory drugs are prescribed only by a doctor; you cannot give them to your child for a long time on your own. Observation continues until growth ends.
- Limiting running, jumping and contact sports during illness
- Physical therapy for abduction and rotation, swimming
- Abduction orthoses and plaster casts according to indications
- Physiotherapy and massage courses prescribed by an orthopedist
- Surgical correction for severe deformity
- Follow-up X-rays every few months